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Neurolymphomatosis

MedGen UID:
1642312
Concept ID:
C4553088
Neoplastic Process
Synonyms: Fowl Paralyses; Fowl Paralysis; Marek disease; Marek's Disease
SNOMED CT: Neurolymphomatosis (766752000)
 
Monarch Initiative: MONDO:0016101
Orphanet: ORPHA206586

Definition

A rare syndrome of peripheral and cranial nerve dysfunction in patients with haematologic malignancies, mostly non-Hodgkin''s lymphoma or acute leukaemia, characterised by painful or painless involvement of peripheral or cranial nerves or nerve roots. The clinical presentation is diverse depending on the site involved and includes plexopathy, mononeuritis multiplex, peripheral neuropathy, radiculopathy and cranial nerve palsies. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVNeurolymphomatosis

Professional guidelines

PubMed

Keddie S, Nagendran A, Cox T, Bomsztyk J, Jaunmuktane Z, Brandner S, Manji H, Rees JH, Ramsay AD, Rossor A, D'Sa S, Reilly MM, Carr AS, Lunn MP
Muscle Nerve 2020 Nov;62(5):617-625. Epub 2020 Sep 10 doi: 10.1002/mus.27045. PMID: 32786031
Baehring JM, Batchelor TT
Cancer J 2012 Sep-Oct;18(5):463-8. doi: 10.1097/PPO.0b013e31826c5ad5. PMID: 23006953

Recent clinical studies

Etiology

Moshe-Lilie O, Ensrud E, Ragole T, Nizar C, Dimitrova D, Karam C
BMC Neurol 2021 Feb 28;21(1):94. doi: 10.1186/s12883-021-02118-7. PMID: 33639867Free PMC Article
Makranz C, Arkadir D, Nachmias B, Gatt ME, Eliahou R, Atlan K, Mordechai A, Goldshmit N, Lossos A
Neurol Sci 2021 May;42(5):1933-1940. Epub 2020 Sep 24 doi: 10.1007/s10072-020-04724-8. PMID: 32974798
Graus F, Dalmau J
Curr Opin Neurol 2013 Oct;26(5):489-95. doi: 10.1097/WCO.0b013e328364c020. PMID: 23892629
Baehring JM, Damek D, Martin EC, Betensky RA, Hochberg FH
Neuro Oncol 2003 Apr;5(2):104-15. doi: 10.1093/neuonc/nop021. PMID: 12672282Free PMC Article
Guberman A, Rosenbaum H, Braciale T, Schlaepfer WW
J Neurol Sci 1978 Mar;36(1):1-12. doi: 10.1016/0022-510x(78)90157-0. PMID: 565805

Diagnosis

Patel DK, Gwathmey KG
Neurol Sci 2022 May;43(5):3019-3038. Epub 2022 Feb 23 doi: 10.1007/s10072-022-05951-x. PMID: 35195810
Makranz C, Arkadir D, Nachmias B, Gatt ME, Eliahou R, Atlan K, Mordechai A, Goldshmit N, Lossos A
Neurol Sci 2021 May;42(5):1933-1940. Epub 2020 Sep 24 doi: 10.1007/s10072-020-04724-8. PMID: 32974798
Lunn MP
Curr Opin Neurol 2019 Oct;32(5):658-665. doi: 10.1097/WCO.0000000000000726. PMID: 31313705
Graus F, Dalmau J
Curr Opin Neurol 2013 Oct;26(5):489-95. doi: 10.1097/WCO.0b013e328364c020. PMID: 23892629
Baehring JM, Batchelor TT
Cancer J 2012 Sep-Oct;18(5):463-8. doi: 10.1097/PPO.0b013e31826c5ad5. PMID: 23006953

Therapy

Terao T, Tsushima T, Ikeda D, Fukumoto A, Kamura Y, Kuzume A, Tabata R, Miura D, Narita K, Takeuchi M, Matsue K
Leuk Lymphoma 2022 Dec;63(14):3394-3401. Epub 2022 Sep 16 doi: 10.1080/10428194.2022.2123239. PMID: 36111741
Yaseen MT, Aziz PAA, Siddique K, Tariq TA
J Coll Physicians Surg Pak 2019 Dec;29(12):S86-S88. doi: 10.29271/jcpsp.2019.12.S86. PMID: 31779751
DeBoer SR, Lesche S, Rodriguez FJ, Ostrow LW
Neurology 2019 Sep 17;93(12):e1229-e1230. doi: 10.1212/WNL.0000000000008131. PMID: 31527110
Bourque PR, Warman Chardon J, Bryanton M, Toupin M, Burns BF, Torres C
Can J Neurol Sci 2018 Mar;45(2):137-143. Epub 2018 Jan 8 doi: 10.1017/cjn.2017.282. PMID: 29307326
Graus F, Dalmau J
Curr Opin Neurol 2013 Oct;26(5):489-95. doi: 10.1097/WCO.0b013e328364c020. PMID: 23892629

Prognosis

Patel DK, Gwathmey KG
Neurol Sci 2022 May;43(5):3019-3038. Epub 2022 Feb 23 doi: 10.1007/s10072-022-05951-x. PMID: 35195810
Makranz C, Arkadir D, Nachmias B, Gatt ME, Eliahou R, Atlan K, Mordechai A, Goldshmit N, Lossos A
Neurol Sci 2021 May;42(5):1933-1940. Epub 2020 Sep 24 doi: 10.1007/s10072-020-04724-8. PMID: 32974798
Briani C, Visentin A, Campagnolo M, Salvalaggio A, Ferrari S, Cavallaro T, Manara R, Gasparotti R, Piazza F
J Peripher Nerv Syst 2019 Mar;24(1):5-18. Epub 2019 Jan 8 doi: 10.1111/jns.12295. PMID: 30556258
Grisold W, Briani C, Vass A
Handb Clin Neurol 2013;115:685-712. doi: 10.1016/B978-0-444-52902-2.00040-0. PMID: 23931810
Baehring JM, Damek D, Martin EC, Betensky RA, Hochberg FH
Neuro Oncol 2003 Apr;5(2):104-15. doi: 10.1093/neuonc/nop021. PMID: 12672282Free PMC Article

Clinical prediction guides

Sato H, Hiroshima S, Anei R, Kamada K
Br J Neurosurg 2023 Aug;37(4):697-700. Epub 2019 Feb 11 doi: 10.1080/02688697.2019.1568391. PMID: 30741017
Terao T, Tsushima T, Ikeda D, Fukumoto A, Kamura Y, Kuzume A, Tabata R, Miura D, Narita K, Takeuchi M, Matsue K
Leuk Lymphoma 2022 Dec;63(14):3394-3401. Epub 2022 Sep 16 doi: 10.1080/10428194.2022.2123239. PMID: 36111741
Ando T, Kamoshita S, Riku Y, Ito A, Ozawa Y, Miyamura K, Fujino M, Ito M, Goto Y, Mano K, Akagi A, Miyahara H, Katsuno M, Yoshida M, Iwasaki Y
Neuropathology 2022 Aug;42(4):295-301. Epub 2022 May 23 doi: 10.1111/neup.12807. PMID: 35607714
Jeong J, Kim SW, Sung DH
J Neurol 2021 Mar;268(3):851-859. Epub 2020 Oct 23 doi: 10.1007/s00415-020-10202-0. PMID: 33098033
Tomita M, Koike H, Kawagashira Y, Iijima M, Adachi H, Taguchi J, Abe T, Sako K, Tsuji Y, Nakagawa M, Kanda F, Takeda F, Sugawara M, Toyoshima I, Asano N, Sobue G
Brain 2013 Aug;136(Pt 8):2563-78. doi: 10.1093/brain/awt193. PMID: 23884813

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